US2008103148A1PendingUtilityA1

Cyclic pyrazinoylguanidine sodium channel blockers

Assignee: PARION SCIENCES INCPriority: Aug 18, 2003Filed: Dec 20, 2007Published: May 1, 2008
Est. expiryAug 18, 2023(expired)· nominal 20-yr term from priority
A61P 7/10A61P 9/12A61P 37/06A61P 43/00A61P 27/02A61P 29/00A61P 27/04A61P 3/12A61P 27/16A61P 17/16A61P 1/18A61P 1/02C07D 401/14C04B 35/632C07D 401/12A61P 11/06C07D 241/26A61P 11/08C07D 417/14C07D 405/14A61P 11/02A61P 1/04C07D 413/12A61P 11/00A61P 15/00C07D 403/12C07D 241/02
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Claims

Abstract

The present invention relates to sodium channel blockers. The present invention also includes a variety of methods of treatment using these inventive sodium channel blockers.

Claims

exact text as granted — not AI-modified
1 - 178 . (canceled)  
     
     
         179 . A method of preventing ventilator-induced pneumonia, comprising administering to a subject an effective of a compound represented by formula (I):  
       
         
           
           
               
               
           
         
       
       wherein 
 X is hydrogen, halogen, trifluoromethyl, lower alkyl, unsubstituted or substituted phenyl, lower alkyl-thio, phenyl-lower alkyl-thio, lower alkyl-sulfonyl, or phenyl-lower alkyl-sulfonyl;  
 Y is hydrogen, hydroxyl, mercapto, lower alkoxy, lower alkyl-thio, halogen, lower alkyl, unsubstituted or substituted mononuclear aryl, or —N(R 2 ) 2 ;  
 R 1  is hydrogen or lower alkyl;  
 each R 2  is, independently, —R 7 , —(CH 2 ) m —OR 8 , —(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —(CH 2 ) n -Z g -R 7 , —(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , or  
                     
 R 3  and R 4  are each, independently, hydrogen, a group represented by formula (A), lower alkyl, hydroxy lower alkyl, phenyl, phenyl-lower alkyl, (halophenyl)-lower alkyl, lower-(alkylphenylalkyl), lower (alkoxyphenyl)-lower alkyl, naphthyl-lower alkyl, or pyridyl-lower alkyl, with the proviso that at least one of R 3  and R 4  is a group represented by formula (A):  
                     
 wherein  
 each R L  is, independently, —R 7 , —(CH 2 ) n —OR 8 , —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 each o is, independently, an integer from 0 to 10;  
 each p is an integer from 0 to 10;  
 with the proviso that the sum of o and p in each contiguous chain is from 1 to 10;  
 each x is, independently, O, NR 10 , C(═O), CHOH, C(═N—R 10 ), CHNR 7 R 10 , or represents a single bond;  
 each R 5  is, independently, —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
  —(CH 2 ) n —NR 12 R 12 , —O—(CH 2 ) m —NR 12 R 12 , —O—(CH 2 ) n —NR 12 R 12 , —O—(CH 2 ) m -(Z) g R 12 , —(CH 2 ) n NR 11 R 11 , O—(CH 2 ) m NR 11 R 11 , (CH 2 ) n —ND-(R 11 ) 3 , —O—(CH 2 ) m —N ⊕ —(R 11 ) 3 , —(CH 2 ) n -(Z) g —(CH 2 ) m —NR 10 R 10 , O—(CH 2 ) m -(Z) g -(CH 2 ) m —NR 10 R 10 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , —(CH 2 ) n —(C═O)NR 12 R 12 , —O—(CH 2 ) m —(C═O)NR 12 R 12 , —O—(CH 2 ) m —(CHOR 8 ) m —CH 2 NR 10 -(Z) g -R 10 , —(CH 2 ) n —(CHOR 8 ) m CH 2 —NR 10 -(Z) g -R 10 , —(CH 2 ) n NR 10 —O(CH 2 ) n (CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 , —O(CH 2 ) n —NR 10 —(CH 2 ) m —(CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 , -(Het)-(CH 2 ) m —OR 8 , -(Het)-(CH 2 ) n —NR 7 R 10 , -(Het)-(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , -(Het)-(CH 2 CH 2 O) m —R 8 , -(Het)-(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , -(Het)-(CH 2 ) m —C(═O)NR 7 R 10 , -(Het)-(CH 2 ) m -(Z) g -R 7 , -(Het)-(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , -(Het)-(CH 2 ) m —CO 2 R 7 , -(Het)-(CH 2 ) m —NR 12 R 12 , -(Het)-(CH 2 ) n —NR 12 R 12 , -(Het)-(CH 2 ) m -(Z) g R 12 , -(Het)-(CH 2 ) m NR 11 R 11 , -(Het)-(CH 2 ) m —N ⊕ —(R 11 ) 3 , -(Het)-(CH 2 ) m -(Z) g -(CH 2 ) m —NR 10 R 10 , -(Het)-(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , -(Het)-(CH 2 ) m —(C═O)NR 12 R 12 , -(Het)-(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , -(Het)-(CH 2 ) m —NR 10 —(CH 2 ) m —(CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 ,  
 wherein when two —CH 2 OR 8  groups are located 1,2- or 1,3- with respect to each other the R 8  groups may be joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 Link-(CH 2 ) n —CAP, Link-(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CAP, Link-(CH 2 CH 2 O) m —CH 2 -CAP, Link-(CH 2 CH 2 O) m —CH 2 CH 2 —CAP, Link-(CH 2 ) n -(Z) g -CAP, Link-(CH 2 ) n (Z) g -(CH 2 ) m —CAP, Link-(CH 2 ) n —NR 13 —CH 2 (CHOR 8 )(CHOR 8 ) n —CAP, Link-(CH 2 ) n —(CHOR 8 ) m CH 2 —NR 13 -(Z) g -CAP, Link-(CH 2 )NR 13 —(CH 2 ) m (CHOR 8 ) n CH 2 NR 13 -(Z) g -CAP, Link-(CH 2 ) m -(Z) g -(CH 2 ) m —CAP, Link-NH—C(═O)—NH—(CH 2 ) m —CAP, Link-(CH 2 ) m —C(═O)NR 13 —(CH 2 ) m —C(═O)NR 10 R 10 , Link-(CH 2 ) m —C(═O)NR 13 —(CH 2 ) m —CAP, Link-(CH 2 ) m —C(═O)NR 11 R 11 , Link-(CH 2 ) m —C(═O)NR 12 R 12 , Link-(CH 2 ) n-(Z) g -(CH 2 ) m -(Z) g -CAP, or Link -Z g -(CH 2 ) m -Het-(CH 2 ) m —CAP;  
 each Link is, independently, —O—, —(CH 2 ) n —, —O(CH 2 ) m —, —NR 13 —C(═O)—NR 13 , —NR 13 —C(═O)—(CH 2 ) m —, —C(═O)NR 13 —(CH 2 ) m , —(CH 2 ) n -Z g -(CH 2 ) n , —S—, —SO—, —SO 2 —, —SO 2 NR 7 —, —SO 2 NR 10 —, or -Het-;  
 each CAP is, independently, thiazolidinedione, oxazolidinedione, heteroaryl-C(═O)N R 13 R 13 , heteroaryl-W, —CN, —O—C(═S)NR 13 R 13 , -Z g R 13 , —CR 10 (Z g R 13 )(Z g R 13 ) n —C(═O)OAr, —C(═O)NR 13 Ar, imidazoline, tetrazole, tetrazole amide, —SO 2 NHR 13 , —SO 2 NH—C(R 13 R 13 )-(Z) g -R 13 , a cyclic sugar or oligosaccharide, a cyclic amino sugar or oligosaccharide,  
                     
 each Ar is, independently, phenyl, substituted phenyl, wherein the substituents of the substituted phenyl are 1-3 substituents independently selected from the group consisting of OH, OCH 3 , NR 13 R 13 , Cl, F, and CH 3 , or heteroaryl;  
 each W is independently, thiazolidinedione, oxazolidinedione, heteroaryl-C(═O)NR 13 R 13 , —CN, —O—C(═S)NR 13 R 13 , -Z g R 13 , —CR 10 (Z g R 13 )(Z g R 13 ) n —C(═O)OAr, —C(═O)NR 13 Ar, imidazoline, tetrazole, tetrazole amide, —SO 2 NHR 13 , —SO 2 NH—C(R 13 R 13 )-(Z) g -R 13 , a cyclic sugar or oligosaccharide, a cyclic amino sugar or oligosaccharide,  
                     
 each R 6  is, independently, —R 5 , —R 7 , —OR 8 , —N(R 7 ) 2 , —(CH 2 ) m —OR 8 , —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 each R 7  is, independently, hydrogen, lower alkyl, phenyl, or substituted phenyl;  
 each R 8  is, independently, hydrogen, lower alkyl, —C(═O)—R 11 , glucuronide, 2-tetrahydropyranyl, or  
                     
 each R 9  is, independently, —CO 2 R 13 , —CON(R 13 ) 2 , —SO 2 CH 2 R 13 , or —C(═O)R 13 ;  
 each R 10  is, independently, —H, —SO 2 CH 3 , —CO 2 R 7 , —C(═O)NR 7 R 9 , —C(═O)R 7 , or —(CH 2 ) m-(CHOH) n —CH 2 OH;  
 each Z is, independently, CHOH, C(═O) n —(CH 2 ) n —, CHNR 13 R 13 , C═NR 13 , or NR 13 ;  
 each R 11  is, independently, lower alkyl;  
 each R 12  is independently, —SO 2 CH 3 , —CO 2 R 13 , —C(═O)NR 13 R 13 , —C(═O)R 13 , or —CH 2 —(CHOH) n —CH 2 OH;  
 each R 13  is, independently, hydrogen, lower alkyl, phenyl, substituted phenyl, —SO 2 CH 3 , —CO 2 R 7 , —C(═O)NR 7 R 7 , —C(═O)NR 7 SO 2 CH 3 , —C(═O)NR 7 —CO 2 R 7 , —C(O)NR 7 —C(═O)NR 7 R 7 , —C(═O)NR 7 —C(═O)R 7 , —C(═O)NR 7 —(CH 2 ) n —(CHOH) n —CH 2 OH, —C(═O)R 7 , or —(CH 2 ) m —(CHOH) n —CH 2 OH, —(CH 2 ) m —NR 7 R 10 ,  
                     
  with the proviso that NR 13 R 13  can be joined on itself to form a group represented by one of the following:  
                     
 each Het is independently, —NR 13 —S—, —SO—, —SO 2 —, —O—, —SO 2 N 13 —, —NHSO 2 —, —NR 13 CO—, or —CONR 13 —;  
 each g is, independently, an integer from 1 to 6;  
 each m is, independently, an integer from 1 to 7;  
 each n is, independently, an integer from 0 to 7;  
 each Q is, independently, —CR 6 R 5 —, —CR 6 R 6 —, —NR 10 , —NR 7 —, —NR 5 —, —S—, —SO— or —SO 2 —,  
 wherein at most three Q in a ring are —NR 10 —, —NR 7 —, —NR 5 —, —S—, —SO— and/or —SO 2 —, at least one Q must be —CR 5 R 6 — or —NR 5 —, and the Q attached to the (C(R L ) 2 ) p — group is —CR 6 R 5  or N;  
 each V is, independently,  
                     
  with the proviso that when V is attached directly to a nitrogen atom, then V can also be, independently, R 7 , R 10 , or (R 11 ) 2 ;  
 with the proviso that, when two —CH 2 OR 8  groups are located 1,2- or 1,3- with respect to each other, the R 8  groups may be joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane;  
 or a pharmaceutically acceptable salt thereof, and  
 inclusive of all enantiomers, diastereomers, and racemic mixtures thereof.  
 
     
     
         180 . The method of  claim 179 , wherein Y is NH 2 , X is Cl, each of R 2 , R 1 , R 3 , R L , and R 6  is H, o is 4, p is 0, and x is a single bond.  
     
     
         181 . The method of  claim 180 , wherein R 5  is 
 —O—(CH 2 ) 4 —OH,    —(CH 2 ) 4 —OH,    —NHSO 2 CH 3 ,    —NH(C═O)CH 3 ,    —CH 2 NH 2 ,    —NH—CO 2 C 2 H 5 ,    —CH 2 NH(C═O)CH 3 ,    —CH 2 NHCO 2 CH 3 ,    —CH 2 NHSO 2 CH 3 ,    —(CH 2 ) 4 —NH 2 ,    —(CH 2 ) 3 —NH 2 ,    —OCH 2 CH 2 NHCO 2 C 2 H 5 ,    —O(CH 2 ) 3 —NH 2 ,    —OCH 2 CH 2 NHSO 2 CH 3 ,    —O—CH 2 CH 2 NH 2 ,    —OCH 2 CHOHCH 2 O-glucuronide,    —OCH 2 CH 2 CHOHCH 2 OH,    —OCH 2 -(α-CHOH) 2 CH 2 OH,    —OCH 2 —(CHOH) 2 CH 2 OH,    —C(═O)NH 2 ,    —O—CH 2 —(C═O)NHCH 2 CHOH,    —O—CH 2 —(C═O)NHCH 2 CHOHCH 2 OH,    —O—CH 2 (C═O)NHCH 2 (CHOH) 2 CH 2 OH,    —O—CH 2 C(C═O)NHSO 2 CH 3 ,    —O—CH 2 (C═O)NHCO 2 CH 3 ,    —O—CH 2 —C(C═O)NH—C(C═O)NH 2 ,    —O—CH 2 —(C═O)NH—(C═O)CH 3 ,    —(C═NH)NH 2 ,    —(CH 2 ) n —NH—C(═NH)—NH 2 ,    —(CH 2 ) 3 —NH—C(═NH)—NH 2 ,    —CH 2 NH—C(═NH)—NH 2 ,    —(CH 2 ) n —CONHCH 2 (CHOH) n —CH 2 OH,    —NH—C(═O)—CH 2 —(CHOH) n CH 2 OH,    —NH—(C═O)—NH—CH 2 (CHOH) 2 CHOH,    —NHC(C═O)NHCH 2 CH 2 OH,    —O—(CH 2 ) m —NH—C(═NH)—N(R 7 ) 2 ,    —O(CH 2 ) 3 —NH—C(═NH)—NH 2 ,    —O—(CH 2 ) m —CHNH 2 —CO 2 NR 7 R 10 ,    —OCH 2 —CHNH 2 —CO 2 NH 2 ,    —NHCH 2 (CHOH) 2 CH 2 OH,    —O—(CH 2 ) n —NH-erythritol,    —O—(CH 2 ) m —NH-sorbitol,    —O—(CH 2 ) m —NH-xylitol,    —O—(CH 2 ) m —NH-glycidol,    —OCH 2 CO 2 H,    —OCH 2 CO 2 C 2 H 5 ,    —O—CH 2 -dioxolane,    —O—(CH 2 ) 3 —OH,    —O—CH 2 —(CHOH) 2 —CH 2 OH,    —O—CH 2 —CHOH—CH 2 OH,    —O—CH 2 CH 2 —O-tetrahydropyran-2-yl,    —O—CH 2 CH 2 OH,    —O—(CH 2 CH 2 O) 4 —CH 3 ,    —O—CH 2 CH 2 OCH 3 ,    —O—CH 2 —(CHOC(═O)CH 3 )—CH 2 —OC(═O)CH 3 ,    —O—(CH 2 CH 2 O) 2 —CH 3 ,    —OCH 2 —CHOH—CHOH—CH 2 OH,                          —O—CH 2 —(CHOH) 2 —CH 2 OH,    ortho —O—CH 2 —CHOH—CH 2 OH,    meta —O—CH 2 —CHOH—CH 2 OH,    —OCH 2 CO 2 H,    —NHCH 2 (CHOH) 2 —CH 2 OH,    —OCH 2 CO 2 Et,    —O—CH 2 C(═O)NH 2 ,    —NHCO 2 Et,    —OCH 2 CH 2 CH 2 CH 2 OH,    —CH 2 NHSO 2 CH 3 ,    —OCH 2 CH 2 CHOHCH 2 OH,    —OCH 2 CH 2 NHCO 2 Et,    —NH—C(═NH 2 )—NH 2 OHOH,    —CH 2 —CHOH—CH 2 —NHBoc,    —O—CH 2 —CHOH—CH 2 —NHBoc,    —OCH 2 CH 2 NHCH 2 (CHOH) 2 CH 2 OH,    —OCH 2 CH 2 NH(CH 2 [(CHOH) 2 CH 2 OH)] 2 ,    —(CH 2 ) 4 —NHBoc,    —OCH 2 CH 2 NHSO 2 CH 3 ,    —(CH 2 ) 3 —NHBoc,    —O—CH 2 —CHOH—CH 2 —NH—C(═NH)—N(R 7 ) 2 ,    —O—(CH 2 ) m —N(SO 2 R 7 ) 2 ,    —(CH 2 ) n —CHNHBocCO 2 R 7  (α),    —O—(CH 2 ) m —CHNHBocCO 2 R 7  (α)    —O—(CH 2 ) 2 —N(Me) 2 ,    —(CH 2 ) n —CHNH 2 CO 2 R 7  (α),    —O—(CH 2 ) m —CHNH 2 CO 2 R 7  (α),    —C(═O)NH—(CH 2 ) m —N(R 10 ) 2 ,    —NHC(═O)(CH 2 ) m —N(R 10 ) 2 ,    —C(═O)NH—(CH 2 ) m —NH—C(═NH)—N(R 7 ) 2 ,    —NH—C(═O)—(CH 2 ) m NH—C(═NH)—N(R 10 ) 2 ,    —O—(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , or    —O—CH 2 —CHOH—CH 2 -guanadine,    
     
     
         182 . The method of  claim 179 , wherein the compound represent by formula (I) is  
       
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
       
     
     
         183 . The method of  claim 179 , wherein the Q attached to the —(C(R L ) 2 ) p  group is N.  
     
     
         184 . The method of  claim 179 , wherein each Q is —CR 6 R 5 — or —CR 6 R 6 — and the Q attached to the —(C(R L ) 2 ) p — group is —CR 6 R 5 .  
     
     
         185 . A method of restoring mucosal defense, comprising administering to a subject an effective of a compound represented by formula (I):  
       
         
           
           
               
               
           
         
       
       wherein 
 X is hydrogen, halogen, trifluoromethyl, lower alkyl, unsubstituted or substituted phenyl, lower alkyl-thio, phenyl-lower alkyl-thio, lower alkyl-sulfonyl, or phenyl-lower alkyl-sulfonyl;  
 Y is hydrogen, hydroxyl, mercapto, lower alkoxy, lower alkyl-thio, halogen, lower alkyl, unsubstituted or substituted mononuclear aryl, or —N(R 2 ) 2 ;  
 R 1  is hydrogen or lower alkyl;  
 each R 2  is, independently, —R 7 , —(CH 2 ) m —OR 8 , —(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —(CH 2 ) n -Z g -R 7 , —(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , or  
                     
 R 3  and R 4  are each, independently, hydrogen, a group represented by formula (A), lower alkyl, hydroxy lower alkyl, phenyl, phenyl-lower alkyl, (halophenyl)-lower alkyl, lower-(alkylphenylalkyl), lower (alkoxyphenyl)-lower alkyl, naphthyl-lower alkyl, or pyridyl-lower alkyl, with the proviso that at least one of R 3  and R 4  is a group represented by formula (A):  
                     
 wherein  
 each R L  is, independently, —R 7 , —(CH 2 )—OR 8 , —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 )—CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) n —R 8 , —(CH 2 CH 2 O) n —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 )_—C(═O)NR 7 R 10 , —O—(CH 2 ) n —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 )—CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 each o is, independently, an integer from 0 to 10;  
 each p is an integer from 0 to 10;  
 with the proviso that the sum of o and p in each contiguous chain is from 1 to 10;  
 each x is, independently, O, NR 10 , C(═O), CHOH, C(═N—R 10 ), CHNR 7 R 10 , or represents a single bond;  
 each R 5  is, independently, —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) n —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 77 —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 —(CH 2 ) n —NR 12 R 12 , —O—(CH 2 ) m —NR 12 R 12 —O—(CH 2 ) n —NR 12 R 12 , O—(CH 2 ) m -(Z) g R 12 , —O—(CH 2 ) n NR 11 R 11 , —O—(CH 2 ) m NR 11 R 11 , —(CH 2 ) n —N ⊕ —(R 11 ) 3 , —O—(CH 2 ) m , —N ⊕ —(R 11 ) 3 , —(CH 2 ) n -(Z) g -(CH 2 ) m —NR 10 R 10 , —O—(CH 2 ) m -(Z) g -(CH 2 ) m —NR 10 R 10 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , —(CH 2 ) n —(C═O)NR 12 R 12 , —O—(CH 2 ) m —(C═O)NR 12 R 12 , —O—(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , (CH 2 ) n —(CHOR 8 ) m CH 2 —NR 10 -(Z) g -R 10 , —(CH 2 ) n NR 10 —O(CH 2 ) m (CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 , —O(CH 2 ) m —NR 10 —(CH 2 ) m —(CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 , -(Het)-(CH 2 ) n —OR 8 , -(Het)-(CH 2 ) m —NR 7 R 10 , -(Het)-(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , -(Het)-(CH 2 CH 2 O) m —R 8 , -(Het)-(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , -(Het)-(CH 2 ) n —C(═O)NR 7 R 10 , -(Het)-(CH 2 ) m -(Z) g -R 7 , -(Het)-(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , -(Het)-(CH 2 ) m —CO 2 R 7 , -(Het)-(CH 2 ) m —NR 12 R 12 , -(Het)-(CH 2 ) n —NR 12 R 12 -(Het)-(CH 2 ) m -(Z) g R 12 , -(Het)-(CH 2 ) m N 11 R 11 , -(Het)-(CH 2 ) m —N ⊕ —(R 11 ) 3 , -(Het)-(CH 2 ) m -(Z) g -(CH 2 ) m —NR 10 R 10 , -(Het)-(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , -(Het)-(CH 2 ) m —(C═O)NR 12 R 12 —(Het)-(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , -(Het)-(CH 2 ) m —NR 10 —(CH 2 ) m —(CHOR 8 ) n CH 2 NR 1 -(Z) g -R 10 ,  
 wherein when two —CH 2 OR 8  groups are located 1,2- or 1,3- with respect to each other the R 8  groups may be joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —O—(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 Link-(CH 2 ) n —CAP, Link-(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CAP, Link-(CH 2 CH 2 O) m —CH 2 -CAP, Link-(CH 2 CH 2 O) m —CH 2 CH 2 —CAP, Link-(CH 2 ) n -(Z) g -CAP, Link-(CH 2 ) n (Z) g -(CH 2 ) m —CAP, Link-(CH 2 ) n —NR 13 —CH 2 (CHOR 8 )(CHOR 8 ) n —CAP, Link-(CH 2 ) n —(CHOR 8 ) m CH 2 —NR 13 -(Z) g -CAP, Link-(CH 2 ) n NR 13 —(CH 2 ) m (CHOR 8 ) n CH 2 NR 13 -(Z) g -CAP, Link-(CH 2 ) m -(Z) g -(CH 2 ) m —CAP, Link-NH—C(═O)—NH—(CH 2 ) m —CAP, Link-(CH 2 ) m —C(═O)NR 13 —(CH 2 ) m —C(═O)NR 10 R 10 , Link-(CH 2 ) n —C(═O)NR 13 —(CH 2 ) m —CAP, Link-(CH 2 ) n —C(═O)NR 11 R 11 , Link-(CH 2 ) m —C(═O)NR 12 R 12 , Link-(CH 2 ) n-(Z) g -(CH 2 ) m -(Z) g -CAP, or Link -Z g -(CH 2 ) m -Het-(CH 2 ) n —CAP;  
 each Link is, independently, —O—, —(CH 2 ) n —, —O(CH 2 ) m —, —NR 13 —C(═O)—NR 13 , —NR 1 —C(═O)—(CH 2 ) m —, —C(═O)NR 13 —(CH 2 ) m , —(CH 2 ) n -Z g -(CH 2 ) n , —S—, —SO—, —SO 2 —, —SO 2 NR 7 —, —SO 2 NR 10 —, or -Het-;  
 each CAP is, independently, thiazolidinedione, oxazolidinedione, heteroaryl-C(═O)N R 13 R 13 , heteroaryl-W, —CN, —O—C(═S)NR 13 R 13 , -Z g R 13 , —CR 10 (Z g R 13 )(Z g R 13 ) n —C(═O)OAr, —C(═O)NR 13 Ar, imidazoline, tetrazole, tetrazole amide, —SO 2 NHR 13 , —SO 2 NH—C(R 13 R 13 )-(Z) g -R 13 , a cyclic sugar or oligosaccharide, a cyclic amino sugar or oligosaccharide,  
                     
 each Ar is, independently, phenyl, substituted phenyl, wherein the substituents of the substituted phenyl are 1-3 substituents independently selected from the group consisting of OH, OCH 3 , NR 13 R 13 , Cl, F, and CH 3 , or heteroaryl;  
 each W is independently, thiazolidinedione, oxazolidinedione, heteroaryl-C(═O)NR 13 R 13 , —CN, —O—C(═S)NR 13 R 13 , -Z g R 13 , —CR 10 (Z g R 13 )(Z g R 13 ) n —C(═O)OAr, —C(═O)NR 13 Ar, imidazoline, tetrazole, tetrazole amide, —SO 2 NHR 13 , —SO 2 NH—C(R 13 R 13 )-(Z) g -R 13 , a cyclic sugar or oligosaccharide, a cyclic amino sugar or oligosaccharide,  
                     
 each R 6  is, independently, —R 5 , —R 7 , —OR 8 , —N(R 7 ) 2 , —(CH 2 ) n —OR 8 , —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) n —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , (CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 each R 7  is, independently, hydrogen, lower alkyl, phenyl, or substituted phenyl;  
 each R 8  is, independently, hydrogen, lower alkyl, —C(═O)—R 11 , glucuronide, 2-tetrahydropyranyl, or  
                     
 each R 9  is, independently, —CO 2 R 13 , —CON(R 13 ) 2 , —SO 2 CH 2 R 13 , or —C(═O)R 13 ;  
 each R 10  is, independently, —H, —SO 2 CH 3 , —CO 2 R 7 , —C(═O)NR 7 R 9 , —C(═O)R 7 , or —(CH 2 ) n —(CHOH) n —CH 2 OH;  
 each Z is, independently, CHOH, C(═O) n —(CH 2 ) n —, CHNR 13 R 13 , C═NR 13 , or NR 13 ;  
 each R 11  is, independently, lower alkyl;  
 each R 12  is independently, —SO 2 CH 3 , —CO 2 R 53 , —C(═O)NR 13 R 13 , —C(═O)R 13 , or —CH 2 —(CHOH) n —CH 2 OH;  
 each R 13  is, independently, hydrogen, lower alkyl, phenyl, substituted phenyl, —SO 2 CH 3 , —CO 2 R 7 , —C(═O)NR 7 R 7 , —C(═O)NR 7 SO 2 CH 3 , —C(═O)NR 7 —CO 2 R 7 , —C(═O)NR 7 —C(═O)NR 7 R 7 , —C(═O)NR 7 —C(═O)R 7 , —C(═O)NR 7 —(CH 2 ) m —(CHOH) n —CH 2 OH, —C(═O)R 7 , or —(CH 2 ) m —(CHOH) n —CH 2 OH, —(CH 2 ) n —NR 7 R 10 ,  
                     
 with the proviso that NR 13 R 13  can be joined on itself to form a group represented by one of the following:  
                     
 each Het is independently, —NR 13 —, —S—, —SO—, —SO 2 —, —O—, —SO 2 NR 13 —, —NHSO 2 —, —NR 13 CO—, or —CONR 13 —;  
 each g is, independently, an integer from 1 to 6;  
 each m is, independently, an integer from 1 to 7;  
 each n is, independently, an integer from 0 to 7;  
 each Q is, independently, —CR 6 R 5 —, —CR 6 R 6 —, —NR 10 —, —NR 7 —, —NR 5 —, —S—, —SO— or —SO 2 —;  
 wherein at most three Q in a ring are —NR 10 —, —NR 7 —, —NR 5 —, —S—, —SO— and/or —SO 2 —, at least one Q must be —CR 5 R 6 — or —NR 5 —, and the Q attached to the —(C(R L ) 2 ) p — group is —CR 6 R 5  or N;  
 each V is, independently,  
                     
  with the proviso that when V is attached directly to a nitrogen atom, then V can also be, independently, R 7 , R 10 , or (R 11 ) 2 ;  
 with the proviso that, when two —CH 2 OR 8  groups are located 1,2- or 1,3- with respect to each other, the R 8  groups may be joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane;  
 or a pharmaceutically acceptable salt thereof, and  
 inclusive of all enantiomers, diastereomers, and racemic mixtures thereof.  
 
     
     
         186 . The method of  claim 185 , wherein Y is N 12 , X is Cl, each of R 2 , R 1 , R 3 , R L , and R 6  is H, o is 4, p is 0, and x is a single bond.  
     
     
         187 . The method of  claim 186 , wherein R 5  is 
 —O—(CH 2 ) 4 —OH,    —(CH 2 ) 4 —OH,    —NHSO 2 CH 3 ,    —NH(C═O)CH 3 ,    —CH 2 NH 2 ,    —NH—CO 2 C 2 H 5 ,    —CH 2 NH(C═O)CH 3 ,    —CH 2 NHCO 2 CH 3 ,    —CH 2 NHSO 2 CH 3 ,    —(CH 2 ) 4 —NH 2 ,    —(CH 2 ) 3 —NH 2 ,    —OCH 2 CH 2 NHCO 2 C 2 H 5 ,    —O(CH 2 ) 3 —NH 2 ,    —OCH 2 CH 2 NHSO 2 CH 3 ,    —O—CH 2 CH 2 NH 2 ,    —OCH 2 CHOHCH 2 O-glucuronide,    —OCH 2 CH 2 CHOHCH 2 OH,    —OCH 2 — (α-CHOH) 2 CH 2 OH,    —OCH 2 —(CHOH) 2 CH 2 OH,    —C(═O)NH 2 ,    —O—CH 2 —(C═O)NHCH 2 CHOH,    —O—CH 2 —(C═O)NHCH 2 CHOHCH 2 OH,    —O—CH 2 (C═O)NHCH 2 (CHOH) 2 CH 2 OH,    —O—CH 2 C(C═O)NHSO 2 CH 3 ,    —O—CH 2 (C═O)NHCO 2 CH 3 ,    —O—CH 2 —C(C═O)NH—C(C═O)NH 2 ,    —O—CH 2 —(C═O)NH—(C═O)CH 3 ,    —(C═NH)NH 2 ,    —(CH 2 ) n —NH—C(═NH)—NH 2 ,    —(CH 2 ) 3 —NH—C(═NH)—NH 2 ,    —CH 2 NH—C(═NH)—NH 2 ,    —(CH 2 ) n —CONHCH 2 (CHOH) n —CH 2 OH,    —NH—C(═O)—CH 2 —(CHOH) n CH 2 OH,    —NH—(C═O)—NH—CH 2 (CHOH) 2 CHOH,    —NHC(C═O)NHCH 2 CH 2 OH,    —O—(CH 2 ) n —NH—C(═NH)—N(R 7 ) 2 ,    —O(CH 2 ) 3 —NE-C(═NH)—NH 2 ,    —O—(CH 2 ) m —CHNH 2 —CO 2 NR 7 R 10 ,    —OCH 2 —CHNH 2 —CO 2 NH 2 ,    —NHCH 2 (CHOH) 2 CH 2 OH,    —O—(CH 2 ) m —NH-erythritol,    —O—(CH 2 ) m —NH-sorbitol,    —O—(CH 2 ) m —NH-xylitol,    —O—(CH 2 ) m —NH-glycidol,    —OCH 2 CO 2 H,    —OCH 2 CO 2 C 2 H 5 ,    —O—CH 2 -dioxolane,    —O—(CH 2 ) 3 —OH,    —O—CH 2 —(CHOH) 2 —CH 2 OH,    —O—CH 2 —CHOH—CH 2 OH,    —O—CH 2 CH 2 —O-tetrahydropyran-2-yl,    —O—CH 2 CH 2 OH,    —O—(CH 2 CH 2 O) 4 —CH 3 ,    —O—CH 2 CH 2 OCH 3 ,    —O—CH 2 —(CHOC(═O)CH 3 )—CH 2 —OC(═O)CH 3 ,    —O—(CH 2 CH 2 O) 2 —CH 3 ,    —OCH 2 —CHOH—CHOH—CH 2 OH,                          —O—CH 2 —(CHOH) 2 —CH 2 OH,    ortho —O—CH 2 —CHOH—CH 2 OH,    meta —O—CH 2 —CHOH—CH 2 OH,    —OCH 2 CO 2 H,    —NHCH 2 (CHOH) 2 —CH 2 OH,    —OCH 2 CO 2 Et,    —O—CH 2 C(═O)NH 2 ,    —NHCO 2 Et,    —OCH 2 CH 2 CH 2 CH 2 OH,    —CH 2 NHSO 2 CH 3 ,    —OCH 2 CH 2 CHOHCH 2 OH,    —OCH 2 CH 2 NHCO 2 Et,    —NH—C(═NNH 2 )—NH 2 OHOH,    —CH 2 —CHOH—CH 2 —NHBoc,    —O—CH 2 —CHOH—CH 2 —NHBoc,    —OCH 2 CH 2 NHCH 2 (CHOH) 2 CH 2 OH,    —OCH 2 CH 2 NH(CH 2 [(CHOH) 2 CH 2 OH)] 2 ,    —(CH 2 ) 4 —NHBoc,    —OCH 2 CH 2 NHSO 2 CH 3 ,    —(CH 2 ) 3 —NHBoc,    —O—CH 2 —CHOH—CH 2 —NH—C(═NH)—N(R 7 ) 2 ,    —O—(CH 2 ) m —N(SO 2 R 7 ) 2 ,    —(CH 2 ) n —CHNHBocCO 2 R 7  (O),    —O—(CH 2 ) m —CHNHBocCO 2 R 7  (<)    —O—(CH 2 ) 2 —N(Me) 2 ,    —(CH 2 ) n —CHNH 2 CO 2 R 7  (α),    —O—(CH 2 ) m —CHNH 2 CO 2 R 7  (α),    —C(═O)NH—(CH 2 ) m —N(R 10 ) 2 ,    —NHC(═O)(CH 2 ) m —N(R 10 ) 2 ,    —C(═O)NH—(CH 2 ) m —NH—C(═NH)—N(R 7 ) 2 ,    —NH—C(═O)—(CH 2 ) m NH—C(═NH)—N(R 10 ) 2 ,    —O—(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , or    —O—CH 2 —CHOH—CH 2 -guanadine,    
     
     
         188 . The method of  claim 185 , wherein the compound represent by formula (I) is  
       
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
       
     
     
         189 . The method of  claim 185 , wherein the Q attached to the —(C(R L ) 2 ) p  group is N.  
     
     
         190 . The method of  claim 185 , wherein each Q is —CR 6 R 5 — or —CR 6 R 6 — and the Q attached to the —(C(R L ) 2 ) p — group is —CR 6 R 5 .  
     
     
         191 . A method of increasing hydration in a mucosal surface of a subject, comprising topically administering to a mucosal surface of a subject an effective amount of a compound represented by formula (I):  
       
         
           
           
               
               
           
         
       
       wherein 
 X is hydrogen, halogen, trifluoromethyl, lower alkyl, unsubstituted or substituted phenyl, lower alkyl-thio, phenyl-lower alkyl-thio, lower alkyl-sulfonyl, or phenyl-lower alkyl-sulfonyl;  
 Y is hydrogen, hydroxyl, mercapto, lower alkoxy, lower alkyl-thio, halogen, lower alkyl, unsubstituted or substituted mononuclear aryl, or —N(R 2 ) 2 ;  
 R 1  is hydrogen or lower alkyl;  
 each R 2  is, independently, —R 7 , —(CH 2 ) m —OR 8 , (CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —(CH 2 ) n -Z g -R 7 , —(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , or  
                     
 R 3  and R 4  are each, independently, hydrogen, a group represented by formula (A), lower alkyl, hydroxy lower alkyl, phenyl, phenyl-lower alkyl, (halophenyl)-lower alkyl, lower-(alkylphenylalkyl), lower (alkoxyphenyl)-lower alkyl, naphthyl-lower alkyl, or pyridyl-lower alkyl, with the proviso that at least one of R 3  and R 4  is a group represented by formula (A):  
                     
 wherein  
 each R L  is, independently, —R 7 , —(CH 2 ) n —OR 8 , —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 7 —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 each o is, independently, an integer from 0 to 10;  
 each p is an integer from 0 to 10;  
 with the proviso that the sum of o and p in each contiguous chain is from 1 to 10;  
 each x is, independently, O, NR 10 , C(═O), CHOH, C(═N—R 10 ), CHNR 7 R 10 , or represents a single bond;  
 each R 5  is, independently, —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) n —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 —(CH 2 ) n —NR 12 R 12 , —O—(CH 2 ) m —NR 12 R 12 , —O—(CH 2 ) n —NR 12 R 12 , —O—(CH 2 ) m -(Z) g R 12 , —(CH 2 ) n NR 11 R 11 , —O—(CH 2 ) m NR 11 R 11 , —(CH 2 ) n —N ⊕ —(R 11 ) 3 , —O—(CH 2 ) m , —N ⊕ —(R 11 ) 3 , —(CH 2 ) n -(Z) g —(CH 2 ) m —NR 10 R 10 , —O—(CH 2 ) m -(Z) g -(CH 2 ) m —NR 10 R 10 , —(CH 2 CH 2 O) n —CH 2 CH 2 NR 12 R 12 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , —(CH 2 ) n —(C═O)NR 12 R 12 , —O—(CH 2 ) m (C═O)NR 12 R 12 , —O—(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) n -R 10 , —(CH 2 ) n —(CHOR 8 ) m CH 2 -(Z) g -R 10 , —(CH 2 ) n NR 10 —O(CH 2 ) m (CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 , —O(CH 2 ) m —NR 10 —(CH 2 ) m —(CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 , -(Het)-(CH 2 ) m —OR 8 , -(Het)-(CH 2 ) m —NR 7 R 10 , -(Het)-(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , -(Het)-(CH 2 CH 2 O) m —R 8 , -(Het)-(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , -(Het)-(CH 2 ) m —C(═O)NR 7 R 10 , -(Het)-(CH 2 ) m -(Z) g -R 7 , -(Het)-(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , -(Het)-(CH 2 ) m —CO 2 R 7 , -(Het)-(CH 2 ) m —NR 12 R 12 , -(Het)-(CH 2 ) n —NR 12 R 12 , -(Het)-(CH 2 ) m -(Z) g R 12 , -(Het)-(CH 2 ) n NR 11 R 11 , -(Het)-(CH 2 ) m —N ⊕ —R 11 ) 3 , -(Het)-(CH 2 ) m -(Z) g -(CH 2 ) m —NR 10 R 10 , -(Het)-(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , -(Het)-(CH 2 ) m —(C═O)NR 12 R 12 , -(Het)-(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , -(Het)-(CH 2 ) m —NR 10 —(CH 2 ) m —(CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 ,  
 wherein when two —CH 2 OR 8  groups are located 1,2- or 1,3- with respect to each other the R 8  groups may be joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —O—(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 Link-(CH 2 ) n —CAP, Link-(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CAP, Link-(CH 2 CH 2 O) m —CH 2 -CAP, Link-(CH 2 CH 2 O) n —CH 2 CH 2 —CAP, Link-(CH 2 ) n -(Z) g -CAP, Link-(CH 2 ) n (Z) g -(CH 2 ) m —CAP, Link-(CH 2 ) n —NR 13 —CH 2 (CHOR 8 )(CHOR 8 ) n —CAP, Link-(CH 2 ) n —(CHOR 8 ) m CH 2 —NR 13 -(Z) g -CAP, Link-(CH 2 ) n NR 13 —(CH 2 ) m (CHOR 8 ) n CH 2 NR 13 -(Z) g -CAP, Link-(CH 2 ) m -(Z) g -(CH 2 ) m —CAP, Link-NH—C(═O)—NH—(CH 2 ) m —CAP, Link-(CH 2 ) m —C(═O)NR 13 —(CH 2 ) m —C(═O)NR 10 R 10 , Link-(CH 2 ) n —C(═O)NR 13 —(CH 2 ) m —CAP, Link-(CH 2 ) m —C(═O)NR 11 R 11 , Link-(CH 2 ) n —C(═O)NR 12 R 12 Link-(CH 2 ) n -(Z) g -(CH 2 ) m -(Z) g -CAP, or Link -Z g -(CH 2 ) m —Het-(CH 2 ) m —CAP;  
 each Link is, independently, —O—, —(CH 2 ) n —, —O(CH 2 ) m —, —NR 13 —C(═O)—NR 13 , —NR 13 —C(═O)—(CH 2 ) m —, —C(═O)NR 13 —(CH 2 ) m , —(CH 2 ) n -Z g -(CH 2 ) n , —S—, —SO—, —SO 2 —, —SO 2 NR 7 —, —SO 2 NR 10 —, or -Het-;  
 each CAP is, independently, thiazolidinedione, oxazolidinedione, heteroaryl-C(═O)N R 13 R 13 , heteroaryl-W, —CN, —O—C(═S)NR 13 R 13 , -Z g R 13 , —CR 10 (Z g R 13 )(Z g R 13 ) n —C(═O)OAr, —C(═O)NR 13 Ar, imidazoline, tetrazole, tetrazole amide, —SO 2 NHR 13 , —SO 2 NH—C(R 13 R 13 )— (Z) g -R 13 , a cyclic sugar or oligosaccharide, a cyclic amino sugar or oligosaccharide,  
                     
 each Ar is, independently, phenyl, substituted phenyl, wherein the substituents of the substituted phenyl are 1-3 substituents independently selected from the group consisting of OH, OCH 3 , NR 13 R 13 , Cl, F, and CH 3 , or heteroaryl;  
 each W is independently, thiazolidinedione, oxazolidinedione, heteroaryl-C(═O)NR 13 R 13 —CN, —O—C(═S)NR 13 R 13 , -Z g R 13 , —CR 10 (Z g R 13 )(Z g R 13 ) n —C(═O)OAr, —C(═O)NR 13 Ar, imidazoline, tetrazole, tetrazole amide, —SO 2 NHR 13 , —SO 2 NH—C(R 13 R 13 )-(Z) g -R 13 , a cyclic sugar or oligosaccharide, a cyclic amino sugar or oligosaccharide,  
                     
 each R 6  is, independently, —R 5 , —R 7 , —OR 8 , —N(R 7 ) 2 , —(CH 2 ) m —OR 8 , —O—(CH 2 ) n —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 77 —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 each R 7  is, independently, hydrogen, lower alkyl, phenyl, or substituted phenyl;  
 each R 8  is, independently, hydrogen, lower alkyl, —C(═O)—R 11 , glucuronide, 2-tetrahydropyranyl, or  
                     
 each R 9  is, independently, —CO 2 R 13 , —CON(R 13 ) 2 , —SO 2 CH 2 R 13 , or —C(═O)R 13 ;  
 each R 10  is, independently, —H, —SO 2 CH 3 , —CO 2 R 7 , —C(═O)NR 7 R 9 , —C(═O)R 7 , or —(CH 2 ) m-(CHOH) n —CH 2 OH;  
 each Z is, independently, CHOH, C(═O) n —(CH 2 ) n —, CHNR 13 R 13 , C═NR 13 , or NR 13 ;  
 each R 11  is, independently, lower alkyl;  
 each R 12  is independently, —SO 2 CH 3 , —CO 2 R 13 , —C(═O)NR 13 R 13 , —C(═O)R 13 , or —CH 2 —(CHOH) n —CH 2 OH;  
 each R 13  is, independently, hydrogen, lower alkyl, phenyl, substituted phenyl, —SO 2 CH 3 , —CO 2 R 7 , —C(═O)NR 7 R 7 , —C(═O)NR 7 SO 2 CH 3 , —C(═O)NR 7 —CO 2 R 7 , —C(═O)NR 7 —C(═O)NR 7 R 7 , —C(═O)NR 7 —C(═O)R 7 , —C(═O)NR 7 —(CH 2 ) m-(CHOH) n —CH 2 OH, —C(═O)R 7 , or —(CH 2 ) m —(CHOH) n —CH 2 OH, —(CH 2 ) m —NR 7 R 10 ,  
                     
 with the proviso that NR 13 R 13  can be joined on itself to form a group represented by one of the following:  
                     
 each Het is independently, —NR 13 —, —S—, —SO—, —SO 2 —, —O—, —SO 2 NR 13 —, —NHSO 2 —, —NR 13 CO—, or —CONR 13 —;  
 each g is, independently, an integer from 1 to 6;  
 each m is, independently, an integer from 1 to 7;  
 each n is, independently, an integer from 0 to 7;  
 each Q is, independently, —CR 6 R 5 —, —CR 6 R 6 —, —NR 10 —, —NR 7 —, —NR 5 —, —S—, —SO— or —SO 2 —,  
 wherein at most three Q in a ring are —NR 10 —, —NR 7 —, —NR 5 —, —S—, —SO— and/or —SO 2 —, at least one Q must be —CR 5 R 6 — or —NR 5 —, and the Q attached to the —(C(R L ) 2 ) p — group is —CR 6 R 5  or N;  
 each V is, independently,  
                     
 with the proviso that when V is attached directly to a nitrogen atom, then V can also be, independently, R 7 , R 10 , or (R 11 ) 2 ;  
 with the proviso that, when two —CH 2 OR 8  groups are located 1,2- or 1,3- with respect to each other, the R 8  groups may be joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane;  
 or a pharmaceutically acceptable salt thereof, and  
 inclusive of all enantiomers, diastereomers, and racemic mixtures thereof.  
 
     
     
         192 . The method of  claim 191 , wherein Y is NH 2 , X is Cl, each of R 2 , R 1 , R 3 , R L , and R 6  is H, o is 4, p is 0, and x is a single bond.  
     
     
         193 . The method of  claim 192 , wherein R 5  is 
 —O—(CH 2 ) 4 —OH,    —(CH 2 ) 4 —OH,    —NHSO 2 CH 3 ,    —NH(C═O)CH 3 ,    —CH 2 NH 2 ,    —NH—CO 2 C 2 H 5 ,    —CH 2 NH(C═O)CH 3 ,    —CH 2 NHCO 2 CH 3 ,    —CH 2 NHSO 2 CH 3 ,    —(CH 2 ) 4 —NH 2 ,    —(CH 2 ) 3 —NH 2 ,    —OCH 2 CH 2 NHCO 2 C 2 H 5 ,    —O(CH 2 ) 3 —NH 2 ,    —OCH 2 CH 2 NHSO 2 CH 3 ,    —O—CH 2 CH 2 NH 2 ,    —OCH 2 CHOHCH 2 O-glucuronide,    —OCH 2 CH 2 CHOHCH 2 OH,    —OCH 2 -(α-CHOH) 2 CH 2 OH,    —OCH 2 —(CHOH) 2 CH 2 OH,    —C(═O)NH 2 ,    —O—CH 2 —(C═O)NHCH 2 CHOH,    —O—CH 2 —(C═O)NHCH 2 CHOHCH 2 OH,    —O—CH 2 (C═O)NHCH 2 (CHOH) 2 CH 2 OH,    —O—CH 2 C(C═O)NHSO 2 CH 3 ,    —O—CH 2 (C═O)NHCO 2 CH 3 ,    —O—CH 2 —C(C═O)NH—C(C═O)NH 2 ,    —O—CH 2 —(C═O)NH—(C═O)CH 3 ,    —(C═NH)NH 2 ,    —(CH 2 ) n —NH—C(═NH)—NH 2 ,    —(CH 2 ) 3 —NH—C(═NH)—NH 2 ,    —CH 2 NH—C(═NH)—NH 2 ,    —(CH 2 ) n —CONHCH 2 (CHOH) m —CH 2 OH,    —NH—C(═O)—CH 2 —(CHOH) n CH 2 OH,    —NH—(C═O)—NH—CH 2 (CHOH) 2 CHOH,    —NHC(C═O)NHCH 2 CH 2 OH,    —O—(CH 2 ) m —NH—C(═NH)—N(R 7 ) 2 ,    —O(CH 2 ) 3 —NH—C(═NH)—NH 2 ,    —O—(CH 2 ) m —CHNH 2 —CO 2 NR 7 R 10 ,    —OCH 2 —CHNH 2 —CO 2 NH 2 ,    —NHCH 2 (CHOH) 2 CH 2 OH,    —O—(CH 2 ) m —NH-erythritol,    —O—(CH 2 ) m —NH-sorbitol,    —O—(CH 2 ) m —NH-xylitol,    —O—(CH 2 ) m —NH-glycidol,    —OCH 2 CO 2 H,    —OCH 2 CO 2 C 2 H 5 ,    —O—CH 2 -dioxolane,    —O—(CH 2 ) 3 —OH,    —O—CH 2 —(CHOH) 2 —CH 2 OH,    —O—CH 2 —CHOH—CH 2 OH,    —O—CH 2 CH 2 —O-tetrahydropyran-2-yl,    —O—CH 2 CH 2 OH,    —O—(CH 2 CH 2 O) 4 —CH 3 ,    —O—CH 2 CH 2 OCH 3 ,    —O—CH 2 —(CHOC(═O)CH 3 )—CH 2 —OC(═O)CH 3 ,    —O—(CH 2 CH 2 O) 2 —CH 3 ,    —OCH 2 —CHOH—CHOH—CH 2 OH,                          —O—CH 2 —(CHOH) 2 —CH 2 OH,    ortho —O—CH 2 —CHOH—CH 2 OH,    meta —O—CH 2 —CHOH—CH 2 OH,    —OCH 2 CO 2 H,    —NHCH 2 (CHOH) 2 —CH 2 OH,    —OCH 2 CO 2 Et,    —O—CH 2 C(═O)NH 2 ,    —NHCO 2 Et,    —OCH 2 CH 2 CH 2 CH 2 OH,    —CH 2 NHSO 2 CH 3 ,    —OCH 2 CH 2 CHOHCH 2 OH,    —OCH 2 CH 2 NHCO 2 Et,    —NH—C(—NH 2 )—NH 2 OHOH,    —CH 2 —CHOH—CH 2 —NHBoc,    —O—CH 2 —CHOH—CH 2 —NHBoc,    —OCH 2 CH 2 NHCH 2 (CHOH) 2 CH 2 OH,    —OCH 2 CH 2 NH(CH 2 [(CHOH) 2 CH 2 OH)] 2 ,    —(CH 2 ) 4 —NHBoc,    —OCH 2 CH 2 NHSO 2 CH 3 ,    —(CH 2 ) 3 —NHBoc,    —O—CH 2 —CHOH—CH 2 —NH—C(═NH)—N(R 7 ) 2 ,    —O—(CH 2 ) m —N(SO 2 R 7 ) 2 ,    —(CH 2 ) n —CHNHBocCO 2 R 7  (α),    —O—(CH 2 ) m —CHNHBocCO 2 R 7  (α)    —O—(CH 2 ) 2 —N(Me) 2 ,    (CH 2 ) n —CHNH 2 CO 2 R 7  (α),    —O—(CH 2 ) m —CHNH 2 CO 2 R 7  (α),    —C(═O)NH—(CH 2 ) m —N(R 10 ) 2 ,    —NHC(═O)(CH 2 ) m —N(R 10 ) 2 ,    —C(═O)NH—(CH 2 ) m —NH—C(═NH)—N(R 7 ) 2 ,    —NH—C(═O)—(CH 2 ) m NH—C(═NH)—N(R 10 ) 2 ,    —O—(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , or    —O—CH 2 —CHOH—CH 2 -guanadine,    
     
     
         194 . The method of  claim 191 , wherein the compound represent by formula (I) is  
       
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
       
     
     
         195 . The method of  claim 191 , wherein the Q attached to the —(C(R L ) 2 ) p  group is N.  
     
     
         196 . The method of  claim 191 , wherein each Q is —CR 6 R 5 — or —CR 6 R 6 — and the Q attached to the —(C(R L ) 2 ) p — group is —CR 6 R 5 .  
     
     
         197 . A method comprising topically administering to a mucosal surface of a subject a compound represented by formula (I):  
       
         
           
           
               
               
           
         
       
       wherein 
 X is hydrogen, halogen, trifluoromethyl, lower alkyl, unsubstituted or substituted phenyl, lower alkyl-thio, phenyl-lower alkyl-thio, lower alkyl-sulfonyl, or phenyl-lower alkyl-sulfonyl;  
 Y is hydrogen, hydroxyl, mercapto, lower alkoxy, lower alkyl-thio, halogen, lower alkyl, unsubstituted or substituted mononuclear aryl, or —N(R 2 ) 2 ;  
 R 1  is hydrogen or lower alkyl;  
 each R 2  is, independently, —R 7 , (CH 2 ) m —OR 8 —(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —(CH 2 ) n -Z g -R 7 , —(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , or  
                     
 R 3  and R 4  are each, independently, hydrogen, a group represented by formula (A), lower alkyl, hydroxy lower alkyl, phenyl, phenyl-lower alkyl, (halophenyl)-lower alkyl, lower-(alkylphenylalkyl), lower (alkoxyphenyl)-lower alkyl, naphthyl-lower alkyl, or pyridyl-lower alkyl, with the proviso that at least one of R 3  and R 4  is a group represented by formula (A):  
                     
 wherein  
 each R L  is, independently, —R 7 , —(CH 2 ) n —OR 8 , —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , (CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 each o is, independently, an integer from 0 to 10;  
 each p is an integer from 0 to 10;  
 with the proviso that the sum of o and p in each contiguous chain is from 1 to 10;  
 each x is, independently, O, NR 10 , C(═O), CHOH, C(═N—R 10 ), CHNR 7 R 10 , or represents a single bond;  
 each R 5  is, independently, —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) n —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2  CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , —O—(CH 2 ) m —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 —(CH 2 ) n —NR 12 R 12 , —O—(CH 2 ) m —NR 12 R 12 , —O—(CH 2 ) n —NR 12 R 12 , —O—(CH 2 ) m -(Z) g R 12 , —(CH 2 ) n NR 11 R 11 , —O—(CH 2 ) m NR 11 R 11 , —(CH 2 ) n —N ⊕ —(R 11 ) 3 , —O—(CH 2 ) m —N ⊕ —(R 1 ) 3 , —(CH 2 ) n -(Z) g —(CH 2 ) m —NR 10 R 10 , —O—(CH 2 ) m -(Z) g -(CH 2 ) m —NR 10 R 10 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , —(CH 2 ) n —(C═O)NR 12 R 12 , —O—(CH 2 ) m —(C═O)NR 12 R 12 , —O—(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , —(CH 2 ) n —(CHOR 8 ) m CH 2 —NR 10 -(Z) g -R 10 , —(CH 2 ) n NR 10 —O(CH 2 ) m (CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 , —O(CH 2 ) m —NR 10 —(CH 2 ) m —(CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 , -(Het)-(CH 2 ) m —OR 8 , -(Het)-(CH 2 ) m —NR 7 R 10 , -(Het)-(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , -(Het)-(CH 2 CH 2 O) m —R 8 , -(Het)-(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , -(Het)-(CH 2 ) m —C(═O)NR 7 R 10 , (Het)-(CH 2 ) m -(Z) g -R 7 , -(Het)-(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , -(Het)-(CH 2 ) m —CO 2 R 7 , -(Het)-(CH 2 ) m —NR 12 R 12 , -(Het)-(CH 2 ) n —NR 12 R 12 , -(Het)-(CH 2 ) m -(Z) g R 12 , -(Het)-(CH 2 ) m NR 11 R 11 , -(Het)-(CH 2 ) m —N ⊕ —(R 11 ) 3 , -(Het)-(CH 2 ) m -(Z) g -(CH 2 ) m —NR 10 R 10 , -(Het)-(CH 2 CH 2 O) m —CH 2 CH 2 NR 12 R 12 , -(Het)-(CH 2 ) m —(C═O)NR 12 R 12 , -(Het)-(CH 2 ) m —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , -(Het)-(CH 2 ) m —NR 10 (CH 2 ) m —(CHOR 8 ) n CH 2 NR 10 -(Z) g -R 10 ,  
 wherein when two —CH 2 OR 8  groups are located 1,2- or 1,3- with respect to each other the R 8  groups may be joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 —O—(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , with the proviso that at least two —CH 2 OR 8  are located adjacent to each other and the R 8  groups are joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane,  
 Link-(CH 2 ) n —CAP, Link-(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CAP, Link-(CH 2 CH 2 O) m —CH 2 -CAP, Link-(CH 2 CH 2 O) m —CH 2 CH 2 —CAP, Link-(CH 2 ) n -(Z) g -CAP, Link-(CH 2 ) n (Z) g -(CH 2 ) m —CAP, Link-(CH 2 ) n —NR 13 —CH 2 (CHOR 8 )(CHOR 8 ) n —CAP, Link-(CH 2 ) n —(CHOR 8 ) m CH 2 —NR 13 -(Z) g -CAP, Link-(CH 2 ) n NR 13 —(CH 2 ) m (CHOR 8 ) n CH 2 NR 13 -(Z) g -CAP, Link-(CH 2 ) m -(Z) g -(CH 2 ) m —CAP, Link-NH—C(═O)—NH—(CH 2 ) m —CAP, Link-(CH 2 ) m —C(═O)NR 13 —(CH 2 ) m —C(═O)NR 10 R 10 , Link-(CH 2 ) m —C(═O)NR 13 —(CH 2 ) m —CAP, Link-(CH 2 ) m —C(═O)NR 11 R 11 , Link-(CH 2 ) m —C(═O)NR 12 R 12 , Link-(CH 2 ) n-(Z) g -(CH 2 ) m -(Z) g -CAP, or Link -Z g -(CH 2 ) m -Het-(CH 2 ) m —CAP;  
 each Link is, independently, —O—, —(CH 2 ) n —, —O(CH 2 ) m —, NR 13 —C(═O)_NR 13 , —NR 13 —C(═O)—(CH 2 ) m —, —C(═O)NR 13 —(CH 2 ) m , —(CH 2 ) n -Z g -(CH 2 ) n , —S—, —SO—, —SO 2 —, —SO 2 NR 7 —, —SO 2 NR 10 —, or -Het-;  
 each CAP is, independently, thiazolidinedione, oxazolidinedione, heteroaryl-C(═O)N R 13 R 13 , heteroaryl-W, —CN, —O—C(═S)NR 13 R 13 , -Z g R 13 , —CR 10 (Z g R 13 )(Z g R 13 ) n —C(═O)OAr, —C(═O)NR 13 Ar, imidazoline, tetrazole, tetrazole amide, —SO 2 NHR 13 , —SO 2 NH—C(R 13 R 13 )-(Z) g -R 13 , a cyclic sugar or oligosaccharide, a cyclic amino sugar or oligosaccharide,  
                     
 each Ar is, independently, phenyl, substituted phenyl, wherein the substituents of the substituted phenyl are 1-3 substituents independently selected from the group consisting of OH, OCH 3 , NR 13 R 13 , Cl, F, and CH 3 , or heteroaryl;  
 each W is independently, thiazolidinedione, oxazolidinedione, heteroaryl-C(═O)NR 13 R 13 —CN, —O—C(═S)NR 13 R 13 , -Z g R 13 , —CR 10 (Z g R 13 )(Z g R 13 ) n —C(═O)OAr, —C(═O)NR 13 Ar, imidazoline, tetrazole, tetrazole amide, —SO 2 NHR 13 , SO 2 NH—C(R 13 R 13 )-(Z) g -R 13 , a cyclic sugar or oligosaccharide, a cyclic amino sugar or oligosaccharide,  
                     
 each R 6  is, independently, —R 5 , —R 7 , —OR 8 , —N(R 7 ) 2 , —(CH 2 ) m —OR 8 , —O—(CH 2 ) m —OR 8 , —(CH 2 ) n —NR 7 R 10 , —O—(CH 2 ) m —NR 7 R 10 , —(CH 2 ) n (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 CH 2 O) m —R 8 , —O—(CH 2 CH 2 O) m —R 8 , —(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —O—(CH 2 CH 2 O) m —CH 2 CH 2 NR 7 R 10 , —(CH 2 ) n —C(═O)NR 7 R 10 , —O—(CH 2 ) m —C(═O)NR 7 R 10 , —(CH 2 ) n -(Z) g -R 7 , —O—(CH 2 ) m -(Z) g -R 7 , —(CH 2 ) n —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —O—(CH 2 ) m —NR 10 —CH 2 (CHOR 8 )(CHOR 8 ) n —CH 2 OR 8 , —(CH 2 ) n —CO 2 R 7 , O—(CH 2 ) m —CO 2 R 7 , —OSO 3 H, —O-glucuronide, —O-glucose,  
                     
 each R 7  is, independently, hydrogen, lower alkyl, phenyl, or substituted phenyl;  
 each R 8  is, independently, hydrogen, lower alkyl, —C(═O)—R 11 , glucuronide, 2-tetrahydropyranyl, or  
                     
 each R 9  is, independently, —CO 2 R 13 , —CON(R 13 ) 2 , —SO 2 CH 2 R 13 , or C(═O)R 13 ;  
 each R 10  is, independently, —H, —SO 2 CH 3 , —CO 2 R 7 , —C(═O)NR 7 R 9 , —C(═O)R 7 , or —(CH 2 ) m-(CHOH) n —CH 2  OH;  
 each Z is, independently, CHOH, C(═O) n —(CH 2 ) n —, CHNR 13 R 13 , C═NR 13 , or NR 13 ;  
 each R 11  is, independently, lower alkyl;  
 each R 12  is independently, —SO 2 CH 3 , —CO 2 R 13 , —C(═O)NR 13 R 13 —C(═O)R 13 , or —CH 2 —(CHOH) n —CH 2 OH;  
 each R 13  is, independently, hydrogen, lower alkyl, phenyl, substituted phenyl, —SO 2 CH 3 , —CO 2 R 7 , —C(═O)NR 7 R 7 , —C(═O)NR 7 SO 2 CH 3 , —C(═O)NR 7 —CO 2 R 7 , —C(═O)NR 7 —C(═O)NR 7 R 7 , —C(═O)NR 7 —C(═O)R 7 , —C(═O)NR 7 —(CH 2 ) n-(CHOH) n —CH 2 OH, —C(═O)R 7 , or —(CH 2 ) n —(CHOH) n —CH 2 OH, —(CH 2 ) n —NR 7 R 10 ,  
                     
  with the proviso that NR 13 R 13  can be joined on itself to form a group represented by one of the following:  
                     
 each Het is independently, —NR 13 —, —S—, —SO—, —SO 2 —, —O—, —SO 2 NR 13 —, —NHSO 2 —, —NR 13 CO—, or —CONR 13 —;  
 each g is, independently, an integer from 1 to 6;  
 each m is, independently, an integer from 1 to 7;  
 each n is, independently, an integer from 0 to 7;  
 each Q is, independently, —CR 6 R 5 —, —CR 6 R 6 —, —NR 10 —, —NR 7 —, —NR 5 —, —S—, —SO— or —SO 2 —;  
 wherein at most three Q in a ring are —NR 10 —, —NR 7 —, —NR 5 —, —S—, —SO— and/or —SO 2 —, wherein at least one Q must be —CR 5 R 6 — or —NR 5 —, and the Q attached to the —(C(R L ) 2 ) p — group is —CR 6 R 5  or N;  
 each V is, independently,  
                     
  with the proviso that when V is attached directly to a nitrogen atom, then V can also be, independently, R 7 , R 1 , or (R 1 ) 2 ;  
 with the proviso that, when two —CH 2 OR 8  groups are located 1,2- or 1,3- with respect to each other, the R 8  groups may be joined to form a cyclic mono- or di-substituted 1,3-dioxane or 1,3-dioxolane;  
 or a pharmaceutically acceptable salt thereof, and  
 inclusive of all enantiomers, diastereomers, and racemic mixtures thereof,  
 whereby hydration of the mucosal surface is increased.  
 
     
     
         198 . The method of  claim 197 , wherein Y is NH 2 , X is Cl, each of R 2 , R 1 , R 3 , R L , and R 6  is H, o is 4, p is 0, and x is a single bond.  
     
     
         199 . The method of  claim 198 , wherein R 1  is 
 —O—(CH 2 ) 4 —OH,    —(CH 2 ) 4 —OH,    —NHSO 2 CH 3 ,    —NH(C═O)CH 3 ,    —CH 2 NH 2 ,    —NH—CO 2 C 2 H 5 ,    —CH 2 NH(C═O)CH 3 ,    —CH 2 NHCO 2 CH 3 ,    —CH 2 NHSO 2 CH 3 ,    —(CH 2 ) 4 —NH 2 ,    —(CH 2 ) 3 —NH 2 ,    —OCH 2 CH 2 NHCO 2 C 2 H 5 ,    —O(CH 2 ) 3 —NH 2 ,    —OCH 2 CH 2 NHSO 2 CH 3 ,    —O—CH 2 CH 2 NH 2 ,    —OCH 2 CHOHCH 2 O-glucuronide,    —OCH 2 CH 2 CHOHCH 2 OH,    —OCH 2 -(α-CHOH) 2 CH 2 OH,    —OCH 2 —(CHOH) 2 CH 2 OH,    —C(═O)NH 2 ,    —O—CH 2 —(C═O)NHCH 2 CHOH,    —O—CH 2 —(C═O)NHCH 2 CHOHCH 2 OH,    —O—CH 2 (C═O)NHCH 2 (CHOH) 2 CH 2 OH,    —O—CH 2 C(C═O)NHSO 2 CH 3 ,    —O—CH 2 (C═O)NHCO 2 CH 3 ,    —O—CH 2 —C(C═O)NH—C(C═O)NH 2 ,    —O—CH 2 —(C═O)NH—(C═O)CH 3 ,    —(C═NH)NH 2 ,    —(CH 2 ) n —NH—C(NH)—NH 2 ,    —(CH 2 ) 3 —NH—C(═NH)—NH 2 ,    —CH 2 NH—C(═NH)—NH 2 ,    —(CH 2 ) n —CONHCH 2 (CHOH) n —CH 2 OH,    —NH—C(═O)—CH 2 —(CHOH) n CH 2 OH,    —NH—(C═O)—NH—CH 2 (CHOH) 2 CHOH,    —NHC(C═O)NHCH 2 CH 2 OH,    —O—(CH 2 ) m —NH—C(═NH)—N(R 7 ) 2 ,    —O(CH 2 ) 3 —NH—C(═NH)—NH 2 ,    —O—(CH 2 ) m —CHNH 2 —CO 2 NR 7 R 10 ,    —OCH 2 —CHNH 2 —CO 2 NH 2 ,    —NHCH 2 (CHOH) 2 CH 2 OH,    —O—(CH 2 ) n —NH-erythritol,    —O—(CH 2 ) m —NH-sorbitol,    —O—(CH 2 ) m —NH-xylitol,    —O—(CH 2 ) m —NH-glycidol,    —OCH 2 CO 2 H,    —OCH 2 CO 2 C 2 H 5 ,    —O—CH 2 -dioxolane,    —O—(CH 2 ) 3 —OH,    —O—CH 2 —(CHOH) 2 —CH 2 OH,    —O—CH 2 —CHOH—CH 2 OH,    —O—CH 2 CH 2 —O-tetrahydropyran-2-yl,    —O—CH 2 CH 2 OH,    —O—(CH 2 CH 2 O) 4 —CH 3 ,    —O—CH 2 CH 2 OCH 3 ,    —O—CH 2 —(CHOC(═O)CH 3 )—CH 2 —OC(═O)CH 3 ,    —O—(CH 2 CH 2 O) 2 —CH 3 ,    —OCH 2 —CHOH—CHOH—CH 2 OH,                          —O—CH 2 —(CHOH) 2 —CH 2 OH,    ortho —O—CH 2 —CHOH—CH 2 OH,    meta —O—CH 2 —CHOH—CH 2 OH,    —OCH 2 CO 2 H,    —NHCH 2 (CHOH) 2 —CH 2 OH,    —OCH 2 CO 2 Et,    —O—CH 2 C(═O)NH 2 ,    —NHCO 2 Et,    —OCH 2 CH 2 CH 2 CH 2 OH,    —CH 2 NHSO 2 CH 3 ,    —OCH 2 CH 2 CHOHCH 2 OH,    —OCH 2 CH 2 NHCO 2 Et,    —NH—C(═NH 2 )—NH 2 OHOH,    —CH 2 —CHOH—CH 2 —NHBoc,    —O—CH 2 —CHOH—CH 2 —NHBoc,    —OCH 2 CH 2 NHCH 2 (CHOH) 2 CH 2 OH,    —OCH 2 CH 2 NH(CH 2 [(CHOH) 2 CH 2 OH)] 2 ,    —(CH 2 ) 4 —NHBoc,    —OCH 2 CH 2 NHSO 2 CH 3 ,    —(CH 2 ) 3 —NHBoc,    —O—CH 2 —CHOH—CH 2 —NH—C(═NH)—N(R 7 ) 2 ,    —O—(CH 2 ) m —N(SO 2 R 7 ) 2 ,    —(CH 2 ) n —CHNHBocCO 2 R 7  (α),    —O—(CH 2 ) m —CHNHBocCO 2 R 7  (α)    —O—(CH 2 ) 2 —N(Me) 2 ,    —(CH 2 ) n —CHNH 2 CO 2 R 7  (α),    —O—(CH 2 ) m —CHNH 2 CO 2 R 7  (α),    —C(═O)NH—(CH 2 ) n —N(R 10 ) 2 ,    —NHC(═O)(CH 2 ) m —N(R 10 ) 2 ,    —C(═O)NH—(CH 2 ) m —NH—C(═NH)—N(R 7 ) 2 ,    —NH—C(═O)—(CH 2 ) m NH—C(═NH)—N(R 10 ) 2 ,    —O—(CH 2 ) n —(CHOR 8 ) m CH 2 NR 10 -(Z) g -R 10 , or    —O—CH 2 —CHOH—CH 2 -guanadine,    
     
     
         200 . The method of  claim 197 , wherein the compound represent by formula (I) is  
       
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
         
           
           
               
               
           
         
       
     
     
         201 . The method of  claim 197 , wherein the Q attached to the —(C(R L ) 2 ) p  group is N.  
     
     
         202 . The method of  claim 197 , wherein each Q is —CR 6 R 5 — or —CR 6 R 6 — and the Q attached to the —(C(R L ) 2 ) p — group is —CR 6 R 5 .

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